Prune Belly syndrome; a complex congenital anomaly of 10 cases from a tertiary hospital

Authors

  • damte shimelis awoke Addis Ababa University

Keywords:

Keywords: Prune Belly Syndrome, cryptorchidism, hydronephrosis, kyphoscoliosis

Abstract

Background: is a rare congenital multisystemic disorder characterized by absence of abdominal wall muscles, dilated urinary bladder, a variety of other urologic abnormalities and undescended testes in males. Patients could have additional pulmonary hypoplasia, a variety of cardiac abnormalities and kyphoscoliosis. Here we present 10 pediatric patients who were on follow up at our renal clinic of the Department of Pediatrics and Child Health of Tikur Anbessa Specialized Teaching Hospital.

 

Author Biography

damte shimelis awoke, Addis Ababa University

Department of Pediatrics and Child Health

References

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Published

2020-12-31