Prune Belly syndrome; a complex congenital anomaly of 10 cases from a tertiary hospital
Keywords:Keywords: Prune Belly Syndrome, cryptorchidism, hydronephrosis, kyphoscoliosis
Background: is a rare congenital multisystemic disorder characterized by absence of abdominal wall muscles, dilated urinary bladder, a variety of other urologic abnormalities and undescended testes in males. Patients could have additional pulmonary hypoplasia, a variety of cardiac abnormalities and kyphoscoliosis. Here we present 10 pediatric patients who were on follow up at our renal clinic of the Department of Pediatrics and Child Health of Tikur Anbessa Specialized Teaching Hospital.
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