Prune Belly syndrome; a complex congenital anomaly of 10 cases from a tertiary hospital


  • damte shimelis awoke Addis Ababa University


Keywords: Prune Belly Syndrome, cryptorchidism, hydronephrosis, kyphoscoliosis


Background: is a rare congenital multisystemic disorder characterized by absence of abdominal wall muscles, dilated urinary bladder, a variety of other urologic abnormalities and undescended testes in males. Patients could have additional pulmonary hypoplasia, a variety of cardiac abnormalities and kyphoscoliosis. Here we present 10 pediatric patients who were on follow up at our renal clinic of the Department of Pediatrics and Child Health of Tikur Anbessa Specialized Teaching Hospital.


Author Biography

damte shimelis awoke, Addis Ababa University

Department of Pediatrics and Child Health


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