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  • Submited: October 1, 2021
  • Published: January 1, 2022


Dermatofibrosarcoma protuberans (DFSP) is a rare soft tissue sarcoma, which arises from the dermis. It behaves as a low to intermediate-grade malignancy, is locally aggressive, and frequently has local recurrence but rarely metastasize. The most common organ of metastasis reported is the lungs. Here we present a rare case of metastasis dermatofibrosarcoma protuberans (DFSP) that presents with intra-abdominal mass causing intestinal obstruction. Exploratory laparotomy and en-bloc resection of the tumor were done followed by adjuvant chemotherapy.


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How to Cite
Zahid, S. K., Wan Muhamad Mokhter , W. M. M. ., Sulaiman , A. F., Wan Zain, W. Z., & Omar, S. Z. (2022). A rare case of intestinal obstruction secondary to metastasis dermatofibrosarcoma protuberans. Ethiopian Medical Journal, 60(01). Retrieved from

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