Imaging findings of head and neck and intracranial sinus histiocytosis with massive lymphadenopathy (Rosai–dorfman disease): A rare case report

Abstract

This case report describes a multifocal involvement of Rosai–Dorfman disease (RDD), which is a benign lymphohistiocytosis, with emphasis on imaging findings in a 19 yrs old Ethiopian female patient who was sent to radiology department at Tikur Anbessa Specialized Hospital (TASH) for head and neck and brain imaging evaluations for an indication of bilateral painless neck swelling of 2 years duration. The head and neck computed tomography (CT) and brain magnetic resonance imaging (MRI) revealed numerous enlarged cervical lymph nodes and soft tissue infiltration of paranasal sinuses with associated lytic osseous changes as well as multiple intracranial extra-axial dural-based masses. Smears of fine needle aspiration biopsy from cervical lymph nodes confirmed the diagnosis of Rosai–Dorfman disease (RDD).