Double Intussusceptions in Peutz-Jeghers Syndrome Patient:: A Case Report
A Case Report
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- Articles
- Submited: December 1, 2023
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Published: January 3, 2024
Abstract
Background: Peutz-Jeghers Syndrome is one of the hereditary gastro-intestinal cancer syndrome with characteristic mucocutaneous pigmentation and histologically distinctive hamartomatous polyps in gastro-intestinal tract. Although it is characteristically benign hamartomatous polyp, majority of affected individuals develop symptoms starting from their second decades. We reported a known Peutz-Jeghers Syndrome case developed recurrent polyps leading to double intussusceptions required bowel resection. Multidisciplinary management and patient compliance to surveillance regime are important in managing PJS patients with potential gastro-intestinal tract complications and relative high risk of developing syndrome specific cancers.
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